AN UNNOTICEABLE ILLNESS THAT KILLS(CONGENITAL INSENSITIVITY TO PAIN WITH ANHIDROSIS- CIPA)

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(Edited)

Good day hivers ! Here is another educative, interesting and perhaps strange health-wise post.

"The history of man is the history of pain" says a popular quote. People are born with pain, and they eventually die in pain and they fight with pain throughout their entire lives. My own definition of pain is quite amazing, pain is how our body tries to communicate with us. When something in our body is in danger or malfunctioning, our body tries to tell us that there's something wrong in that area. But what do you think will happen if our body doesn't tell us that? Such people that doesn't feel pain are suffering from CIPA.

CIPA means CONGENITAL INSENSITIVITY TO PAIN WITH ANHIDROSIS. A CIPA patient doesn't feel pain or temperature no matter how little it may be. He can get cut, get stitches without no anaesthetics, break his bones, and rupture his organs but he still won't feel any pain. When a normal person feels pain, his or her heart rate changes and the ANI figure suddenly goes down but, CIPA patient shows a steady graph which means he cannot feel the change in temperature. His brain can't receive any signals even when his body gets stimulated.

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Injured eyes: Sourced from pixabay

Food has no taste in his mouth. He doesn't have to freeze, but he feels no warmth either. If he had a brain tumor, he would have had no headaches. Even if he suffered a brain hemorrhage after a fall, he would have felt no symptoms. The illness is incurable but can only be maintained. It is hereditary and the carrier rarely live longer than 20 years. Patients with CIPA has a ticking bomb inside of them which could explode anytime, Boom !

I think doctors share a similarity with detectives of a serious crime squad. The culprits are the illnesses that attack patients while the doctors are the detectives who need to find them. One day, they met a criminal that is very hard to catch. He doesn't say a word, and something the doctors haven't identifies slowly begins to attack from inside.

The illness that i'm talking about is Congenital Insensitivity to Pain with Anhidrosis (CIPA). With this illness, the criminal is silent. It numbs the senses and ability to feel pain. Patients bite on and bite off their tongue once they grow teeth. Their hands and feet's are repeatedly injured and deformed. They rub their eyes to the point where they damage their corneas. Despite losing pieces of tongue and tearing their corneas, they don't feel pain, so they can't stop these actions. They're also less able to secrete sweat to lower their body temperate, so more than 50% die before three of a fever.

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Charcot joints are shown in this boy with CIPA. His right knee and right ankle are enlarged and distorted. The skin over the medial aspect of the ankle is darkened with a draining wound secondary to superimposed osteomyelitis; By Author: Sourced from Wikipedia Under Creative Commons

CAUSE
The main cause of CIPA is genetic mutations. Patients who have CIPA inherited it from their parents.

SYMPTOMS
Signs in CIPA is observed from childhood. The commons symptoms are:

  • Inability to sweat.
  • Inability to regulate their body temperature.
  • Inability to feel pain and temperature.
  • Bones problem and joint problem due to repeated injuries.

TREATMENT
There is no actual treatment for CIPA patients but, there are some preventive measures to be taken into consideration.

  • Checking their vitals is as important as their life.
  • Fixing of CCTV camera to the room where they sleep so as to monitor their actions at night. In case of any action that may be injurious to their health, they will see it the next morning and know what to do as well.
  • They are advised to go for medical checkup regularly.

Thanks for visiting my blog ❗

References

Indo, Y; Pagon, RA; Adam, MP; Ardinger, HH; Wallace, SE; Amemiya, A; Bean, LJH; Bird, TD; Ledbetter, N; Mefford, HC; Smith, RJH; Stephens, K (1993). "Congenital Insensitivity to Pain with Anhidrosis".

Mutations in the TRKA/NGF Receptor Gene in Patients with Congenital Insensitivity to Pain with Anhidrosis

Shatzky S, Moses S, Levy J, et al. (June 2000). "Congenital insensitivity to pain with anhidrosis (CIPA) in Israeli-Bedouins: genetic heterogeneity, novel mutations in the TRKA/NGF receptor gene, clinical findings, and results of nerve conduction studies". Am. J. Med. Genet. 92 (5): 353–60.

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